International Journal of Hematology and Oncology
2023, Vol 33, Num 4 Page(s): 094-099
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RHABDOMYOSARCOMA OF THE COMMON BILE DUCT: CASE REPORT
Deniz TUĞCU1, Ferhan AKICI1, Arzu AKÇAY1, Zafer ŞALCIOĞLU1, Gönül AYDOĞAN1, Hülya ŞEN1, Serdar YEŞİNEL1, Zerrin ÖNAL2, Mahir GÜLCAN2, Gülay TİRELİ3, Murat ÖNAL3, Güngör TEKOĞUL4, Rana RAMAZANOĞLU5, Sergülen DERVİŞOĞLU5
1Bakırköy Doğumevi, Kadın-Doğum ve Çocuk Hastalıkları Eğitim Hastanesi Hematoloji-Onkoloji Servisi
2Bakırköy Doğumevi, Kadın-Doğum ve Çocuk Hastalıkları Eğitim Hastanesi Gastroenteroloji Servisi
3Bakırköy Doğumevi, Kadın-Doğum ve Çocuk Hastalıkları Eğitim Hastanesi Çocuk Cerrahi Servisi
4Bakırköy Doğumevi, Kadın-Doğum ve Çocuk Hastalıkları Eğitim Hastanesi Radyoloji Birimi
5İstanbul Üniversitesi Cerrahpaşa Tıp Fakültesi, Patoloji Ana Bilim Dalı, İSTANBUL
Keywords: Rhabdomyosarcoma, Bilier system, Childhood
Rhabdomyosarcoma of the common bile duct is one of the rare causes of biliary tract obstruction in childhood. Nevertheless it is the most common cause of obstructive jaundice due to neoplastic biliary obstruction. A 2 year-9 month-old boy was admitted to our hospital with cholestatic jaundice. In his examination, it was revealed a mass derived from common bile duct. The diagnosis of rhabdomyosarcoma was established, after histopathological examination of this mass. Subtotal excision, hepaticojejunostomy and Roux-en-Y anastomosis were performed. Chemotherapy consisting of vincristine, actinomycin-D and cosmogen was administered. Radiotherapy was also given. Nine months after therapy, gastrointestinal bleeding and peritonitis carcinomatosa were detected. After that chemotherapy regimen was changed to ifosfamid and etoposid. Although it was rare, rhabdomyosarcoma of common bile duct should be considered in differantial diagnosis of cholestatic jaundice.
Deniz TUĞCU1, Ferhan AKICI1, Arzu AKÇAY1, Zafer ŞALCIOĞLU1, Gönül AYDOĞAN1, Hülya ŞEN1, Serdar YEŞİNEL1, Zerrin ÖNAL2, Mahir GÜLCAN2, Gülay TİRELİ3, Murat ÖNAL3, Güngör TEKOĞUL4, Rana RAMAZANOĞLU5, Sergülen DERVİŞOĞLU5
1Bakırköy Doğumevi, Kadın-Doğum ve Çocuk Hastalıkları Eğitim Hastanesi Hematoloji-Onkoloji Servisi
2Bakırköy Doğumevi, Kadın-Doğum ve Çocuk Hastalıkları Eğitim Hastanesi Gastroenteroloji Servisi
3Bakırköy Doğumevi, Kadın-Doğum ve Çocuk Hastalıkları Eğitim Hastanesi Çocuk Cerrahi Servisi
4Bakırköy Doğumevi, Kadın-Doğum ve Çocuk Hastalıkları Eğitim Hastanesi Radyoloji Birimi
5İstanbul Üniversitesi Cerrahpaşa Tıp Fakültesi, Patoloji Ana Bilim Dalı, İSTANBUL
Keywords: Rhabdomyosarcoma, Bilier system, Childhood
Rhabdomyosarcoma of the common bile duct is one of the rare causes of biliary tract obstruction in childhood. Nevertheless it is the most common cause of obstructive jaundice due to neoplastic biliary obstruction. A 2 year-9 month-old boy was admitted to our hospital with cholestatic jaundice. In his examination, it was revealed a mass derived from common bile duct. The diagnosis of rhabdomyosarcoma was established, after histopathological examination of this mass. Subtotal excision, hepaticojejunostomy and Roux-en-Y anastomosis were performed. Chemotherapy consisting of vincristine, actinomycin-D and cosmogen was administered. Radiotherapy was also given. Nine months after therapy, gastrointestinal bleeding and peritonitis carcinomatosa were detected. After that chemotherapy regimen was changed to ifosfamid and etoposid. Although it was rare, rhabdomyosarcoma of common bile duct should be considered in differantial diagnosis of cholestatic jaundice.
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